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KMID : 0882420130840060868
Korean Journal of Medicine
2013 Volume.84 No. 6 p.868 ~ p.872
Pneumatosis Cystoides Intestinalis with Pneumoperitoneum Complicating Systemic Sclerosis: A Case Report
Im Jae-Uk

Kim Eun-Hye
Jun Hong-Gil
Oh Ji-Seon
Choi Seung-Won
Kang Byeong-Seong
Abstract
The gastrointestinal tract is commonly involved in patients with systemic sclerosis. The manifestations include motility disorder, pseudo-obstruction, malabsorption, bacterial overgrowth, diverticuli, and, less commonly, pneumatosis cystoides intestinalis (PCI). PCI is characterized by the presence of air in the submucosal or subserosal layer of the bowel wall and is often accompanied by pneumoperitoneum. Although PCI is a benign condition that often responds to conservative management, it is a poor prognostic factor of systemic sclerosis. We report a case of PCI in a patient with systemic sclerosis. The chest and abdominal radiographic findings comprised pneumoperitoneum, marked dilation of the bowels, and intramural air, compatible with PCI. The patient¡¯s symptoms improved spontaneously. It is important to recognize PCI as a gastrointestinal manifestation of systemic sclerosis, and physicians should differentiate it from serious complications-such as intestinal perforation-based on clinical manifestations.
KEYWORD
Pneumatosis cystoides intestinalis, Pneumoperitoneum, Systemic sclerosis
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